{"id":16523,"date":"2019-07-12T14:06:39","date_gmt":"2019-07-12T14:06:39","guid":{"rendered":"https:\/\/www.elza-institute.com\/?p=16523"},"modified":"2020-09-27T13:14:59","modified_gmt":"2020-09-27T13:14:59","slug":"can-cross-linking-cxl-treat-terrien-marginal-degeneration-tmd","status":"publish","type":"post","link":"https:\/\/www.elza-institute.com\/pt\/can-cross-linking-cxl-treat-terrien-marginal-degeneration-tmd\/","title":{"rendered":"O Cross-Linking (CXL) pode tratar a Degeneresc\u00eancia Marginal de Terrien (DTM)?"},"content":{"rendered":"<h5><strong>O que \u00e9 a Degeneresc\u00eancia Marginal de Terrien?<\/strong><\/h5>\n<p>Surpreendentemente, pouco se sabe sobre as causas da degeneresc\u00eancia marginal de Terrien (DTM). O que sabemos \u00e9 que: \u00e9 rara, tr\u00eas em cada quatro pessoas afectadas s\u00e3o homens; o seu in\u00edcio ocorre normalmente entre a terceira e a quinta d\u00e9cada de vida e, na maioria das vezes, ambos os olhos s\u00e3o afectados.<\/p>\n<p>Sabemos mais sobre a patologia: a doen\u00e7a \u00e9 caracterizada pelo adelga\u00e7amento da margem (bordos) da c\u00f3rnea onde esta se encontra com a parte branca do olho (a escler\u00f3tica). O afinamento come\u00e7a normalmente na parte superior da margem, progride e envolve toda a circunfer\u00eancia da periferia da c\u00f3rnea. A doen\u00e7a resulta normalmente no crescimento de novos vasos sangu\u00edneos - neovasculariza\u00e7\u00e3o - e na forma\u00e7\u00e3o de cicatrizes e dep\u00f3sitos de l\u00edpidos (normalmente vistos como opacidades estromais pontuais finas e amareladas) na margem. \u00c0 medida que a degeneresc\u00eancia progride, conduz normalmente a um aumento do astigmatismo contra a regra ou obl\u00edquo. A c\u00f3rnea pode ficar gravemente enfraquecida, podendo ocorrer rupturas espont\u00e2neas da membrana de Descemet que resultam em l\u00edquido interlamelar ou quistos da c\u00f3rnea. Embora a perfura\u00e7\u00e3o espont\u00e2nea seja rara, mesmo um pequeno traumatismo pode perfurar a c\u00f3rnea. A quest\u00e3o \u00e9: como \u00e9 que a DTM pode ser tratada?<\/p>\n<p>At\u00e9 h\u00e1 pouco tempo, n\u00e3o havia muito que se pudesse fazer, para al\u00e9m de tentar controlar o astigmatismo dos doentes com \u00f3culos ou lentes r\u00edgidas perme\u00e1veis ao g\u00e1s e monitorizar cuidadosamente o afinamento da c\u00f3rnea. Mas se a c\u00f3rnea se torna t\u00e3o fina que a perfura\u00e7\u00e3o \u00e9 iminente, ent\u00e3o o transplante de c\u00f3rnea \u00e9 o pr\u00f3ximo passo l\u00f3gico - embora, dado o facto de a doen\u00e7a ser de natureza perif\u00e9rica e os transplantes de c\u00f3rnea terem de se estender \u00e0 periferia da c\u00f3rnea... o sucesso do tratamento pode ser extremamente dif\u00edcil de alcan\u00e7ar.<\/p>\n<p>No entanto, h\u00e1 outra abordagem que pode ajudar.<\/p>\n<h5><strong>A Degeneresc\u00eancia Marginal de Terrien pode ser reticulada?<\/strong><\/h5>\n<p>O reticulado da c\u00f3rnea (CXL) pode tratar com sucesso as ectasias da c\u00f3rnea (doen\u00e7as de afinamento) como o ceratocone, a ectasia p\u00f3s-LASIK e o derretimento da c\u00f3rnea. Pensa-se que a liga\u00e7\u00e3o cruzada das prote\u00ednas (principalmente colag\u00e9nio) no estroma da c\u00f3rnea n\u00e3o s\u00f3 fortalece a c\u00f3rnea, como tamb\u00e9m a torna mais resistente \u00e0 digest\u00e3o enzim\u00e1tica. Se o CXL pode parar o derretimento da c\u00f3rnea (uma carater\u00edstica da DTM), poder\u00e1 tamb\u00e9m impedir a progress\u00e3o da DTM?<\/p>\n<p>Sim. Trat\u00e1mos com sucesso v\u00e1rios doentes com DTM utilizando CXL, aplicado na \u00e1rea de afinamento m\u00e1ximo da c\u00f3rnea, e utilizando uma esponja para cobrir e proteger o limbo corneano da ilumina\u00e7\u00e3o UV. Verific\u00e1mos que o CXL, utilizando o Protocolo de Dresden, padr\u00e3o-ouro, n\u00e3o s\u00f3 melhora a forma da c\u00f3rnea destes doentes, a acuidade visual e a qualidade, como tamb\u00e9m inverte o afinamento da c\u00f3rnea que ocorreu nas \u00e1reas ect\u00e1sicas perif\u00e9ricas fundidas das c\u00f3rneas destes doentes.<\/p>\n<p>A melhor explica\u00e7\u00e3o para estes resultados \u00e9 o facto de o CXL aumentar a resist\u00eancia do estroma da c\u00f3rnea \u00e0 digest\u00e3o enzim\u00e1tica. Em condi\u00e7\u00f5es normais, existe uma homeostase - um equil\u00edbrio fino - entre a s\u00edntese e a degrada\u00e7\u00e3o do colag\u00e9nio da c\u00f3rnea. Aparentemente, o CXL, ao dificultar a degrada\u00e7\u00e3o do colag\u00e9nio, altera o equil\u00edbrio para a s\u00edntese, o que explicaria as melhorias na espessura da c\u00f3rnea destes doentes observadas at\u00e9 \u00e0 data. Um tratamento bem sucedido com CXL tem a vantagem adicional de evitar a necessidade de queratoplastia - ajudando a preservar o escasso tecido da c\u00f3rnea e poupando o doente aos riscos e ao exigente regime de col\u00edrio p\u00f3s-procedimento que \u00e9 parte integrante dos procedimentos de transplante da c\u00f3rnea.<\/p>\n<p>Estes resultados implicam tamb\u00e9m uma outra utiliza\u00e7\u00e3o do CXL na DTM: a profilaxia. Ao contr\u00e1rio do ceratocone em adultos, que come\u00e7a e p\u00e1ra de progredir, e onde o CXL s\u00f3 \u00e9 indicado para utiliza\u00e7\u00e3o quando se observa progress\u00e3o, a DTM tende a continuar a progredir inexoravelmente. O CXL realizado no in\u00edcio da evolu\u00e7\u00e3o da DTM pode ajudar a travar a progress\u00e3o da doen\u00e7a precocemente, preservando a vis\u00e3o e talvez poupando as pessoas \u00e0 necessidade de utilizar lentes r\u00edgidas perme\u00e1veis ao g\u00e1s ou a algumas das manifesta\u00e7\u00f5es posteriores da doen\u00e7a.<\/p>\n<p>&nbsp;<\/p>\n<div id=\"attachment_16528\" class=\"wp-caption aligncenter\">\n<img fetchpriority=\"high\" decoding=\"async\" class=\"alignnone wp-image-16528 size-full\" src=\"https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terriens-OCT.jpg\" alt=\"\" width=\"814\" height=\"583\" aria-describedby=\"caption-attachment-16528\" srcset=\"https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terriens-OCT.jpg 814w, https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terriens-OCT-300x215.jpg 300w, https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terriens-OCT-768x550.jpg 768w\" sizes=\"(max-width: 814px) 100vw, 814px\" \/><\/p>\n<p id=\"caption-attachment-16528\" class=\"wp-caption-text\" style=\"text-align: center;\">Esta imagem de OCT mostra um afinamento da c\u00f3rnea na periferia (os bordos) da c\u00f3rnea)<\/p>\n<\/div>\n<div id=\"attachment_16527\" class=\"wp-caption aligncenter\">\n<img decoding=\"async\" class=\"aligncenter wp-image-16527 size-large\" src=\"https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terrien-OS-1024x681.png\" alt=\"\" width=\"800\" height=\"532\" aria-describedby=\"caption-attachment-16527\" srcset=\"https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terrien-OS-1024x681.png 1024w, https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terrien-OS-300x200.png 300w, https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terrien-OS-768x511.png 768w, https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terrien-OS-1080x718.png 1080w, https:\/\/www.elza-institute.com\/wp-content\/uploads\/2019\/07\/Terrien-OS.png 1609w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/><\/p>\n<p id=\"caption-attachment-16527\" class=\"wp-caption-text\" style=\"text-align: center;\">Este mapa de topografia da c\u00f3rnea mostra que a DTM do paciente resultou numa assimetria significativa da c\u00f3rnea e, consequentemente, em astigmatismo.<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>A Degeneresc\u00eancia Marginal de Terrien (DTM) \u00e9 um afinamento progressivo da c\u00f3rnea nos seus bordos, junto \u00e0 escler\u00f3tica (a parte branca do olho). O cross-linking corneano (CXL) pode tratar a DTM como pode tratar outras doen\u00e7as de afinamento da c\u00f3rnea, como o ceratocone? Para o descobrir, clique na liga\u00e7\u00e3o para ler mais!<\/p>","protected":false},"author":1,"featured_media":16526,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[214,95],"tags":[],"class_list":["post-16523","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-farhad-hafezi","category-scientific-article"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Can Cross-Linking (CXL) treat Terrien\u2019s Marginal Degeneration (TMD)? - The ELZA Institute, Dietikon ZH<\/title>\n<meta name=\"description\" content=\"Terrien\u2019s Marginal Degeneration (TMD) is a progressive thinning of the cornea at its edges. It&#039;s not keratoconus, but it is an ectasia. And CXL can treat it\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.elza-institute.com\/pt\/kann-cross-linking-cxl-die-marginale-hornhautdegeneration-nach-terrien-behandeln\/\" \/>\n<meta property=\"og:locale\" content=\"pt_PT\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Can Cross-Linking (CXL) treat Terrien\u2019s Marginal Degeneration (TMD)? - The ELZA Institute, Dietikon ZH\" \/>\n<meta property=\"og:description\" content=\"Terrien\u2019s Marginal Degeneration (TMD) is a progressive thinning of the cornea at its edges. It&#039;s not keratoconus, but it is an ectasia. 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